Zida - Matenda
Muyezo
Choyamba, chizindikiro cha chizindikiro. Zizindikiro ziyenera kukhala zobwerezabwereza komanso za episodic, ndipo ziyenera kukhala ndi ziwalo ziwiri kapena zingapo. Kuphatikizika kodziwika bwino kumaphatikizapo khungu ndi m'mimba, kapena mtima ndi kupuma. Vuto lokhazikika pamakina amodzi, kapena lomwe limakhazikika m'malo mosinthasintha, silikugwirizana.
Chachiwiri, umboni weniweni wa kutulutsidwa kwa mast cell mediator. Izi zikutanthawuza kuyeza kwa labotale - nthawi zambiri kukwera kwa seramu tryptase panthawi yoyerekeza ndi momwe wodwalayo alili wopanda zizindikiro, kapena ma metabolites okwera m'mkodzo. Mlingo wa tryptase womwe umagwiritsidwa ntchito nthawi zambiri ndi kukwera kosachepera 20% pamwamba pazoyambira kuphatikiza 2 ng/mL yowonjezera.
Chachitatu, kuyankha ku chithandizo choloza ma mast cell. Kupititsa patsogolo kwa H1 ndi H2 antihistamines, mast cell stabilizers, kapena othandizira okhudzana nawo amathandizira kuzindikira. Mulingo uwu umanyamula kulemera kwenikweni muzochita, makamaka pamene kuyesa kwa mkhalapakati sikunatsimikizike.
Kuphatikiza pa izi, zinthu zina zomwe zimatha kupanga chithunzi chomwechi siziyenera kuphatikizidwa - kuphatikiza mastocytosis, yomwe imaphatikizapo kuchuluka kwenikweni kwa mast cell ndipo amafufuzidwa mosiyana. Dziwani kuti kusiyanasiyana kwa chimangochi kulipo ndipo akatswiri amasiyana momwe amagwiritsira ntchito muyeso wachiwiri; njira ya dokotala ikhoza kusiyana ndi zomwe zafotokozedwa apa.
Zofunikira zonse zitatu, palimodzi. Wachiwiri - umboni wotsimikizika - ndipamene maulendo ambiri ozindikira matenda amayimitsidwa, ndipo nthawi zambiri pazifukwa zaukadaulo osati chifukwa chakuti wodwalayo alibe vutoli.
Serum tryptase ndiye chikhomo chokhazikika kwambiri. Pamafunika miyeso iwiri kuti imasuliridwe: Imodzi imatengedwa panthawi kapena pambuyo pa zomwe zachitika, ndipo ina imatengedwa poyambira zizindikiro zikakhala chete. Phindu limodzi lodzipatula ndilovuta kuchitapo kanthu, chifukwa chofunika ndi kusintha kuchokera pa chiyambi cha munthu osati nambala yeniyeni. Zitsanzo za pachimake ziyenera kujambulidwa mkati mwa ola limodzi kapena anayi kuchokera pamene zayamba, ndipo zitsanzo zoyambira pasanathe maola 24 zizindikiro zitakhazikika.
Kusonkhanitsa mkodzo wa maola 24 kuyeza mkhalapakati metabolites - nthawi zambiri N-methylhistamine, prostaglandin D2 kapena metabolite yake 11-beta-prostaglandin F2-alpha, ndi leukotriene E4. Izi zimatenga zenera lalitali kuposa kutulutsa magazi kamodzi ndipo zimatha kuzindikira kuyambitsa komwe chithunzi chitha kuphonya. Ayenera kuyambika pa nthawi ya zizindikiro.
Zofunikira pakuwongolera ndizokhazikika, ndipo ndizomwe zimapangitsa kuti zotsatira zake zibwerere molakwika. Ambiri mwa oyimira pakatiwa ndi osakhazikika kutentha kwa chipinda. Zitsanzo zimafunika kuziziritsidwa nthawi yomweyo, kuziziritsa nthawi yonse yosonkhanitsa, ndikukonzedwa mwachangu. Zitsanzo za Prostaglandin ndizosalimba kwambiri. Chitsanzo chosiyidwa pa kauntala, kapena chotumizidwa ndi zoyendera wamba, chikhoza kutulutsa zotsatira zabwinobwino kuchokera kwa wodwala yemwe anali kuchitapo kanthu.
Pachifukwa ichi, ndikofunikira kutsimikizira ndondomeko yoyendetsera ntchito ndi dokotala wolamula ndi labotale kale kusonkhanitsa m'malo motsatira zotsatira zosayembekezereka. Sikuti ma laboratories aliwonse amayesa izi pafupipafupi, ndipo si zida zonse zotolera zomwe zimafika ndi malangizo okwanira.
Musanayesere
Kutanthauzira
Mayesowa amayesa mankhwala okhala ndi moyo waufupi. Trypase ifika pachimake mkati mwa maola angapo achitapo kanthu kenako ndikugwa; ma metabolites a mkodzo amakhalabe nthawi yayitali koma amawonetsabe zenera lochepa. Ngati chitsanzocho chatengedwa pakati pa zigawo, sipangakhale kanthu kokwezeka kuti tipeze - osati chifukwa kutsegula sikunachitike, koma chifukwa sikungathekenso kuyezedwa.
Kuyesa kwa mkhalapakati kolakwika sikungoletsa MCAS - ndikumvetsetsa chifukwa chake kumalepheretsa kukhumudwa kosayenera.
Mayesowa amayesa mankhwala okhala ndi moyo waufupi. Trypase ifika pachimake mkati mwa maola angapo achitapo kanthu kenako ndikugwa; ma metabolites a mkodzo amakhalabe nthawi yayitali koma amawonetsabe zenera lochepa. Ngati chitsanzocho chatengedwa pakati pa zigawo, sipangakhale kanthu kokwezeka kuti tipeze - osati chifukwa kutsegula sikunachitike, koma chifukwa sikungathekenso kuyezedwa.
Mavuto ogwirira ntchito omwe afotokozedwa pamwambapa amawonjezera izi. Pakati pa kusonkhanitsa molakwika ndi zitsanzo zowonongeka, gawo lalikulu la zotsatira zoipa m'mabuku ndi m'maakaunti a odwala ndizolephera luso m'malo mopanda matenda enieni.
Palibe mwa izi zikutanthauza kuti kuyesa kuyenera kudumpha. Umboni wotsimikizika umalimbitsa kuzindikiridwa, umatsegula mwayi wolandira chithandizo, komanso nkhani za inshuwaransi ndi malo ogona. Zikutanthauza kuti zotsatira zabwinobwino ziyenera kuyambitsa kukambirana za nthawi ndi kagwiridwe kake - ndipo mwina kuyesanso kubwereza poyankha - m'malo motseka funso.
Bweretsani mbiri yazizindikiro yolembedwa yokonzedwa ndi organ system m'malo motsatira nthawi. Kulemba zizindikiro za khungu, m'mimba, zamtima, kupuma, ndi zamitsempha monga magulu zimapangitsa kuti machitidwe ambiri awoneke nthawi yomweyo, kumene nkhani yofotokozera imakonda kubisa.
Bweretsani zolemba zanu zoyambira ngati mwasunga imodzi - onani Zoyambitsa za zomwe mungalembe. Nkhani zolembedwa zokhala ndi nthawi komanso kuuma mtima zimapatsa dokotala china chake choti agwiritse ntchito, ndikuthandizira kukhazikitsa mawonekedwe a zochitika zomwe muyeso woyamba umafunikira.
Bweretsani zotsatira zoyezetsa zam'mbuyo, kuphatikizirapo zoyipa. Mapanelo odziwika bwino, ma endoscopies osadabwitsa, komanso zolimbitsa thupi zomveka bwino za mtima ndizodziwitsa: ndi gawo la njira yopatula, ndipo amapewa kubwereza mayeso omwe achitika kale.
Funsani mwachindunji za nthawi yoyesera mkhalapakati ndi kasamalidwe ka zitsanzo. Ndi funso lololera, limasonyeza kuti mukumvetsa ndondomekoyi, ndipo limapangitsa kuti mwayi wopeza zotsatira zabwino.
Bweretsani zotulukapo zoyezetsa kale, kuphatikizirapo zomwe mulibe. Mapanelo odziwika bwino, ma endoscopies osadabwitsa, komanso zolimbitsa thupi zomveka bwino za mtima ndizodziwitsa: ndi gawo la njira yopatula, ndipo amapewa kubwereza mayeso omwe achitika kale.